A surgical shunt combined with heart medicines for children with severe lung high blood pressure

This is a research study for children aged 6 months to 18 years with severe pulmonary artery hypertension—a serious condition where blood pressure in the lungs becomes dangerously high. The study compares two groups: children who receive a surgical procedure called a Potts-shunt along with standard medicines, and children who receive only the standard medicines. The goal is to see whether the combination of surgery and medication helps children feel better, grow normally, and avoid needing a lung transplant over 3 years of follow-up.

Even when children take multiple heart medications for severe pulmonary hypertension, many still get worse and may need a lung transplant. Doctors want to know if adding a surgical procedure can help these children do better and stay healthier for longer.