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Hereditary Attr AmyloidosisJanuary 2021Summary reviewed May 2026

An IV Infusion Stopped Nerve Damage Progression in Hereditary Amyloidosis Patients

This long-term extension followed 211 people with hereditary transthyretin amyloidosis who continued patisiran, an IV RNA-silencing infusion, for up to a year. People who started on patisiran kept their nerve function steady; those who switched from inactive comparison began to improve.

What the trial was testing

The trial enrolled 211 patients with hereditary attr amyloidosis. The study was sponsored by Alnylam Pharmaceuticals and tracked outcomes across the full group of patients who matched the trial's eligibility profile.

It was a large trial designed to confirm whether the treatment works well enough for wider use. Trials at this stage are designed to produce evidence regulators and physicians can act on — not just observations to follow up later.

What the results showed

Nerve function held steady or improved on long-term patisiran treatment.

The Lancet Neurology · 2021 · NCT02510261

These findings — that stable or improved nerve function on long-term patisiran in hereditary ATTR amyloidosis — were published in the The Lancet Neurology and represent the headline result of the study.

Researchers tracked outcomes across 211 patients enrolled in the trial. The result was consistent enough across the group that the team felt confident reporting it.

What this means for patients

For patients with hereditary attr amyloidosis, this result changes the calculus on what to ask their care team about. Whether it changes day-to-day care depends on factors like disease subtype, prior treatments, and where the patient is in their care journey.

What you can do now

Patisiran (Onpattro) is FDA-approved and available now for hereditary ATTR amyloidosis with nerve symptoms. It is given as an IV infusion every three weeks. A newer related drug, vutrisiran (Amvuttra), is also approved and given as a quarterly subcutaneous injection. Ask a neurologist about treatment for confirmed ATTR amyloidosis.

Eligibility for the treatments mentioned above depends on specific test results and clinical history. Bring this summary, the trial name, and your most recent labs or pathology report to your next visit.

Open hereditary attr amyloidosis trials

RecruitingObservational study

The Italian Transthyretin Amyloidosis Web-Network

The study aims, by generating a large registry of patients with ATTR amyloidosis, including data at diagnosis and during follow up, to describe the natural history of ATTR amyloidosis in a real-world setting and to define and validate prognostic models, response criteria applicable at any point of the disease. The registry will also be used for data sharing and to allow the possibility of a close collaboration amongst the amyloidosis experts of the ARTC and all the physicians around the Country involved in the diagnosis and management of systemic amyloidosis. Thanks to the online registry, the diagnostic facility of the ARTC will be made available to requesting physicians.

Legnano, MI, Italy +24 more
RecruitingObservational study

Early Diagnosis of Age-Linked CArdiac TransThyRetin Amyloidosis by Selective Screening in Spinal Stenosis Surgery

The goal of this observational study is to keep track of the cardiological follow-up of patients who have undergone back surgery because of symptomatic narrowing of the spinal canal and in whom microscopic examination of the tissue removed during this surgery showed a high amount of local deposits of small proteins. This finding may be an early sign of a condition in which other organs (especially the heart) may also be affected by these proteins, called amyloidosis. Patients who participate in this study, will be followed up for life. During the first routine consultation with the cardiologist, the physician-investigator will collect information, such as demographics (age, weight, height, gender), medical history, medication, symptoms and the results of prescribed examinations. These examinations include microscopic examination of tissue removed during the surgery, blood tests, electrocardiography, echocardiography and a bone scan. These examinations are clinically necessary and appropriate, and patients should undergo them even without participating in the study.

Bruges, Belgium